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Tuberous Sclerosis With Intracranial Aneurysm
Steven Beall, MD;
Peyton Delaney, MD
Arch Neurol. 1983;40(13):826-827.
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| Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings. |
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The classic renal lesion in tuberous sclerosis (TS) is angiomyolipoma with aneurysmal formation in the interlobar arteries. Aneurysms of cerebral vessels in TS have been found only twice.1,2 We report a third case that suggests that renal and intracranial aneurysms in TS may represent a common defect.
REPORT OF A CASE
A 17-year-old girl had major motor seizures for seven years. At age 12 years, she had an IQ of 80. A maternal aunt also had seizures. New symptoms of déjà vu followed by right focal motor seizures prompted hospitalization. An adenoma sebaceum, pitting of her teeth, and one shagreen patch were noted. Neurologic examination showed a visual acuity of 20/20 OD, 20/30 OS, a Marcus Gunn's pupillary sign OS with optic pallor, and a left inferior altitudinal defect. A computed tomographic scan revealed periventricular calcifications and an enhancing lesion in the left parasellar region (Fig 1). Cerebral angiograms
. . . [Full Text PDF of this Article]
Author Affiliations
From the Department of Medicine, Division of Neurology, University of Texas Health Science Center, San Antonio.
Footnotes
Accepted for publication April 21, 1983.
Reprint requests to Department of Medicine, Division of Neurology, University of Texas Health Science Center, San Antonio, TX 78284 (Dr Delaney).
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