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Peggy A. Hanson, MD; Lewis P. Rowland, MD

Arch Neurol. 1971;24(1):31-39.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

CONGENITAL facial diplegia, or Möbius syndrome, is usually considered to be a static disorder. Recently, however, there have been reports of myotonic dystrophy presenting with facial weakness in the newborn period.^1,2; some cases of Möbius syndrome may therefore be due to progressive disease. We recently encountered three children diagnosed originally as Möbius syndrome but with a progressive myopathy resembling facioscapulohumeral (FSH) dystrophy, an association not previously delineated.

Report of Cases

CASE 1.—A female infant was born after normal gestation and delivery and weighed 2,860 gm (6 lb 4 oz). She was bottle-fed but had difficulty sucking. From birth, the mother noticed a lack of facial expression, and the child was unable to close her eyes or mouth fully. Her early development was otherwise normal, and she walked at 14 months. The facial disorder became more conspicuous. At age 9, because of disfiguring progressive pouting of the lips, she . . . [Full Text PDF of this Article]

Author Affiliations
Philadelphia

From the Neurological Clinical Research Center and the Spiller Neurological Unit, Hospital of the University of Pennsylvania, Philadelphia.

Footnotes
Accepted for publication July 20, 1970.

Reprint requests to Albany Medical College, Department of Neurology and Pediatrics, Albany, NY 12208 (Dr. Hanson).

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