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Mohsen Mahloudji, MD; Khosrow Daneshbod, (Mechanic), MD; Manouchehr Karjoo, MD

Arch Neurol. 1970;22(4):294-298.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

VAN BOGAERT and Bertrand,¹ who were mainly responsible for the delineation of familial spongy degeneration of the brain as a nosological entity, have recently published a monograph covering the historical background and reviewing the literature up to 1966. They discuss the various features of the syndrome in full. The purpose of the present communication is to report a family from Iran, to bring the literature up to date, and to review critically the genetic aspects of the disorder.

Report of a Case

A 14-month-old girl was admitted into hospital with the chief complaint of fever, cough, and convulsions for eight days. She was the product of an uneventful pregnancy and fullterm delivery. She appeared normal at birth. From 1 month of age her mother noticed irritability and continual crying, suspecting "the family disease." She was unable to hold her head and was generally limp. At about 3 months . . . [Full Text PDF of this Article]

Author Affiliations
Shiraz, Iran

From the departments of neurology (Dr. Mahloudji), pathology (Dr. Daneshbod [Mechanic] ), and pediatrics (Dr. Karjoo), Pahlavi University and Nemazee Hospital, Shiraz, Iran.

Footnotes
Submitted for publication Oct 8, 1969; accepted Oct 24.

Reprint requests to Nemazee Hospital, Shiraz, Iran (Dr. Mahloudji).

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