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OFTEN FAMILIAL STARTING IN THE FEET AND LEGS AND LATER REACHING THE HANDS.

J. M. Charcot; p. Martin

Arch Neurol. 1967;17(5):553-557.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

I

Progressive muscular atrophy seems to subdivide into secondary groups, which increase in number as clinical observation becomes more attentive and more precise.

The form of muscular atrophy that constitutes the subject of this work seems to present characteristics sufficiently definite and stable to merit a special description and a place of its own in nosology.

During the past year, we had occasion to observe five patients with this affliction. It is from their symptoms that we shall describe the disease. We shall also have recourse, when necessary, to analogous observations published by other authors

[Five case reports follow.]

II

Now we can try to assemble all the information furnished by these five cases and group them and coordinate them so that a nosologie description emerges containing the main traits of the clinical picture, always so similar in each case. These are the essential points that, in our opinion, distinguish this form of muscular atrophy: . . . [Full Text PDF of this Article]

Footnotes
Translation of: Sur une forme particuliére d'atrophie musculaire progressive souvent familiale débutant par les pieds et les jambes et atteignant plus tard les mains, Revue de Médecine6:97-138, 886.

Messrs. Landouzy and Dejerine (Concerning Progressive Attophic Myopathy, Revue de Médecine, 1885, p. 354 and following), commenting on Eichhorst's, Hammonds's and Ormerod's cases, considered them myopathic and classified them in their outline of muscular atrophies as Eichhorst's femoral-tibial type. This point of view seemed warranted by the interpretation of symtomatology and of evolution reported by Eichhorst as well as by the hereditary character of the atrophies. We explained above why the examination of cases at the Salpêtriére does not allow us to accept the nosologic interpretation proposed by Messrs. Landouzy and Dejerine. As for the word femoral-tibial, it seems inadequate to characterize the clinical aspects of this affliction in which the alteration of the femoral musculature is, as a whole, quite secondary, while that of the foot and hand muscles deserves special notice. We also think that the name of Eichhorst should not be retained, since Eulenburg's observation precedes Eichhorst's by 17 years and is not inferior in the study of the affected muscles. Moreover, the idea of heredity is also mentioned by Eulenburg.

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