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Vincenzo Di Lazzaro, MD; Fabio Pilato, MD; Michele Dileone, MD; Giacomo Minicuci, MD; Paolo Profice, MD; Cesare Colosimo, MD; Tommaso Tartaglione, MD; Pietro A. Tonali, MD

Arch Neurol. 2007;64(2):284-285.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Cerebrospinal fluid pulsation in patients with Marfan syndrome may dilate the dural sac, causing dural ectasia. This condition, which may be identified in more than 90% of patients, is considered a specific sign of the disease and is usually asymptomatic.¹ Rarely, dural ectasia is associated with sacral arachnoid cysts, which may cause lumbosacral root compression with pain and sphincteric disturbance.² Herein, we report a 25-year-old man with Marfan syndrome who presented with a 2-year history of worsening distal sensory motor deficits of the lower limbs. Clinical examination showed bilateral clawfoot (Figure 1) with weakness of the distal muscles and hypoesthesia below the L4 level. Electromyography showed denervation in the distal lower limb muscles. Magnetic resonance imaging of the spine showed a large . . . [Full Text of this Article]

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