Divry-Van Bogaert syndrome. Clinical and ultrastructural findings

G. Bussone, E. A. Parati, A. Boiardi, L. La Mantia, M. Savoiardo, R. Boeri and G. Tredici

A case of a progressive disease with epilepsy, marble skin, and roentgenographic evidence of tapering of the distal carotid branches with corticomeningeal angiomatosis was studied. The clinical course, angiographic findings, and skin biopsy results justified the diagnosis of noncalcifying venous capillary angiomatosis, or Divry-Van Bogaert syndrome.