This Article  • References  • Full text PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Contact me when this article is cited  Related Content  • Similar articles in this journal

A Case Report

Emre Kokmen, MD; James K. Billman, Jr, MD; Murray R. Abell, MD, PhD

Arch Neurol. 1977;34(12):782-784.

Abstract
• A 38-year-old man developed pain and peripheral-type weakness on the right side of his face and was discovered to have decreased hearing bilaterally, as well as optic nerve swelling on the right. The pain and optic nerve swelling subsided over a period of six weeks, but hearing loss and facial weakness persisted. Thirty months later, he developed dysphagia, ataxia, dysarthria, nystagmus, and progressive spastic quadriparesis. He died approximately four years after the onset of the illness. Although no evidence of disease was found other than in the central nervous system during life, two nodules in the right lower lung were found on autopsy. The examination of these nodules, as well as the brain stem, showed an angiocentric and angionecrotic process with lymphoreticular and plasmacytoid invasion.

Author Affiliations
From the Departments of Neurology (Dr Kokmen) and Pathology (Drs Billman and Abell), University of Michigan Medical School, Ann Arbor.

Footnotes
Accepted for publication April 25, 1977.

Reprint requests to Department of Neurology, University of Michigan Medical School, Ann Arbor, MI 48109 (Dr Kokmen).