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Report of Two Families

W. C. Wiederholt, MD

Arch Neurol. 1974;30(3):252-254.

Abstract
Based on findings from two patients with hereditary brachial neuropathy and their families, an autosomal dominant mode of inheritance with high penetrance is suggested. The first attack usually occurs before age 20. Most patients have several attacks, infrequently more than four. The likelihood of further episodes of neuropathy decreases with age. Longrange prognosis is good except for occasional minor neurological deficits usually involving proximal muscles of the upper extremities. Based on electromyographic and nerve conduction studies, patients with this disorder do not appear to have a generalized neuropathy. The clinical picture of hereditary brachial neuropathy is indistinguishable from nonfamilial brachial plexus neuropathy except for earlier onset, recurrence of attacks, and family history.

Author Affiliations
San Diego, Calif

From the Veterans Administration Hospital and Department of Neurosciences, University of California, San Diego.

Footnotes
Accepted for publication Sept 11, 1973.

Reprint requests to VA Hospital, 3350 LaJolla Village Dr, San Diego, CA 92161 (Dr. Wiederholt).

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