This Article  • References  • Full text PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Citation map  • Citing articles on HighWire  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

Presentation of Three Cases With Features Resembling Spinocerebellar Degeneration

William Sheramata, MD; H. Stephen Kott, MD; Donat P. Cyr, MD

Arch Neurol. 1971;25(4):289-294.

Abstract
Three patients with Chediak-Higashi-Steinbrinck syndrome and clinical pictures resembling a spinocerebellar degeneration are older than any patients previously reported. Including this report, six of 38 cases in the English literature have presented evidence of similar neurologic pictures. Pathologic evidence of reported cases and animal work support the conclusion that a form of spinocerebellar degeneration is, to some extent, a regular part of the varied clinical and pathologic manifestations comprising this syndrome.

Author Affiliations
Boston

From the departments of neurology and internal medicine, Lahey Clinic Foundation, Boston. Dr. Sheramata is now with the Boston City Hospital.

Footnotes
Accepted for publication March 30, 1970.

Reprint requests to Department of Neurology, Lahey Clinic Foundation, 605 Commonwealth Ave, Boston 02215 (Dr. Kott).

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?

THIS ARTICLE HAS BEEN CITED BY OTHER ARTICLES

Chediak-Higashi Syndrome: Neurologic Appearance
Pettit and Berdal
Arch Neurol 1984;41:1001-1002.
ABSTRACT