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Prion Diseases

Citations 1-10 of 42 total displayed.

Most recent content (1 Apr 2008):

Observations
In Vivo Detection of Thalamic Gliosis: A Pathoradiologic Demonstration in Familial Fatal Insomnia
Stéphane Haïk; Damien Galanaud; Marius G. Linguraru; Katell Peoc’h; Nicolas Privat; Baptiste A. Faucheux; Nicholas Ayache; Jean-Jacques Hauw; Didier Dormont; Jean-Philippe Brandel
Arch Neurol 2008; 65: 545-549. [Abstract] [Full text] [PDF]  

Past content (since Jun 1998):

Observations
Creutzfeldt-Jakob Disease, Prion Protein Gene Codon 129VV, and a Novel PrPSc Type in a Young British Woman
Simon Mead; Susan Joiner; Melanie Desbruslais; Jonathan A. Beck; Michael O’Donoghue; Peter Lantos; Jonathan D. F. Wadsworth; John Collinge
Arch Neurol 2007; 64: 1780-1784. [Abstract] [Full text] [PDF]  

Observations
Novel Prion Protein Conformation and Glycotype in Creutzfeldt-Jakob Disease
Gianluigi Zanusso; Alberto Polo; Alessia Farinazzo; Romolo Nonno; Franco Cardone; Michele Di Bari; Sergio Ferrari; Serena Principe; Matteo Gelati; Elisa Fasoli; Michele Fiorini; Frances Prelli; Blas Frangione; Giuseppe Tridente; Marina Bentivoglio; Alessandra Giorgi; Maria Eugenia Schininà; Bruno Maras; Umberto Agrimi; Nicola Rizzuto; Maurizio Pocchiari; Salvatore Monaco
Arch Neurol 2007; 64: 595-599. [Abstract] [Full text] [PDF]  

Images in Neurology
Creutzfeldt-Jakob Disease With Focal Electroencephalographic and Magnetic Resonance Imaging Findings
K. Meng Tan; Gregory A. Worrell; Joseph E. Parisi; Daniel H. Lachance
Arch Neurol 2007; 64: 600-601. [Extract] [Full text] [PDF]  

Observations
Colorado Surveillance Program for Chronic Wasting Disease Transmission to Humans: Lessons From 2 Highly Suspicious but Negative Cases
C. Alan Anderson; Patrick Bosque; Christopher M. Filley; David B. Arciniegas; B. K. Kleinschmidt-DeMasters; W. John Pape; Kenneth L. Tyler
Arch Neurol 2007; 64: 439-441. [Abstract] [Full text] [PDF]  

Images in Neurology
Early Abnormality of Diffusion-Weighted Magnetic Resonance Imaging Followed by Brain Atrophy in a Case of Gerstmann-Sträussler-Scheinker Disease
Shiro Yamamoto; Makoto Kinoshita; Satoshi Furukawa; Koji Kajiyama
Arch Neurol 2007; 64: 450-451. [Extract] [Full text] [PDF]  

Original Contributions
Influence of Homozygosity for Methionine at Codon 129 of the Human Prion Gene on the Onset of Neurological and Hepatic Symptoms in Wilson Disease
Uta Merle; Wolfgang Stremmel; Reinhard Geßner
Arch Neurol 2006; 63: 982-985. [Abstract] [Full text] [PDF]  

Observations
Childhood Onset in Familial Prion Disease With a Novel Mutation in the PRNP Gene
Ekaterina Rogaeva; Cindy Zadikoff; Jonathan Ponesse; Gerold Schmitt-Ulms; Toshitaka Kawarai; Christine Sato; Shabnam Salehi-Rad; Peter St. George-Hyslop; Anthony E. Lang
Arch Neurol 2006; 63: 1016-1021. [Abstract] [Full text] [PDF]  

Original Contributions
Clinical Features and Diagnosis of the MM2 Cortical Subtype of Sporadic Creutzfeldt-Jakob Disease
Anna Krasnianski; Bettina Meissner; Walter Schulz-Schaeffer; Kai Kallenberg; Mario Bartl; Uta Heinemann; Daniela Varges; Hans A. Kretzschmar; Inga Zerr
Arch Neurol 2006; 63: 876-880. [Abstract] [Full text] [PDF]  

Correspondence
Interleukin 4 and Interleukin 10 in Creutzfeldt-Jakob Disease—Reply
Katharina Stoeck; Inga Zerr
Arch Neurol 2006; 63: 911-a. [Extract] [Full text] [PDF]  

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